Dermatofibrosarcoma Protuberans

Dermatofibrosarcoma Protuberans

Dermatofibrosarcoma Protuberans (DFSP) is a rare type of skin cancer that begins in the middle layer of the skin, known as the dermis. It is characterized by slow-growing tumors that can invade surrounding tissues.

Causes and Risk Factors

The exact cause of DFSP is not known, but it is often associated with specific genetic mutations. Risk factors may include previous radiation exposure or certain genetic conditions.

Symptoms

Symptoms of DFSP typically include a painless, firm lump or mass on the skin that may appear reddish or purplish. The tumor may grow slowly over time and may become raised or protuberant.

Diagnosis

Diagnosis of DFSP involves a biopsy to examine tissue under a microscope. Imaging tests such as MRI or CT scans may be used to determine the extent of the tumor and assess if it has spread.

Treatment

Treatment for DFSP typically involves surgery to remove the tumor with a wide margin of healthy tissue. In some cases, additional treatments such as radiation therapy or targeted therapy may be recommended to reduce the risk of recurrence.